Article
Current status of sporadic and neurofibromatosis type 1-associated malignant peripheral nerve sheath tumors.
Current oncology reports - 1 Jul 2009
Widemann Brigitte C
Abstract excerpt
Malignant peripheral nerve sheath tumors (MPNSTs) are highly aggressive soft tissue sarcomas that rarely occur in the general population but have a lifetime incidence of 8% to 13% in those with neurofibromatosis type 1 (NF1). Complete surgical resection is the standard treatment for MPNSTs. Unresectable MPNSTs carry a poor prognosis, and survival appears to be worse in NF1-associated tumors than in sporadic...
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.
