Article
Studies in haemoglobin E beta-thalassaemia.
British journal of haematology - 1 May 2008
Olivieri Nancy F, Muraca Giulia M, O'Donnell Angela, Premawardhena Anuja, Fisher Christopher, Weatherall David J
Abstract excerpt
Haemoglobin E beta-thalassaemia is the commonest form of severe thalassaemia in many Asian countries, but little is known about its natural history, the reasons for its clinical diversity, or its optimal management. Despite its frequency, haemoglobin E beta-thalassaemia is often managed in an ill-defined and haphazard way, usually by demand transfusion. We studied a cohort of Sri Lankan patients with haemoglobin...
Topics
- Adolescent
- Adult
- Child
- Child, Preschool
- Hemoglobin E
- Humans
- Middle Aged
- Phenotype
- Practice Guidelines as Topic
- Sri Lanka
- beta-Thalassemia
