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Article

The development of behavioral abnormalities in the motor neuron degeneration (mnd) mouse.

Brain research - 24 May 2002

Bolivar Valerie J, Scott Ganus J, Messer Anne

Abstract excerpt

The motor neuron degeneration (mnd) mouse, which has widespread abnormal accumulating lipoprotein and neuronal degeneration, has a mutation in CLN8, the gene for human progressive epilepsy with mental retardation (EPMR). EPMR is one of the neuronal ceroid lipofuscinoses (NCLs), a group of neurological disorders characterized by autofluorescent lipopigment accumulation, blindness, seizures, motor deterioration,...

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Source

Identifiers

PMID: 12020865
DOI: 10.1016/s0006-8993(02)02470-8

Genes

CLN8
NCL

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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