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Article

An early-onset congenic strain of the motor neuron degeneration (mnd) mouse.

Molecular genetics and metabolism - 1 Apr 1999

Messer A, Manley K, Plummer J A

Abstract excerpt

The mouse mutant motor neuron degeneration (mnd/mnd) has been proposed as a model of neuronal ceroid lipofuscinosis (NCL) on the basis of widespread abnormal accumulating lipopigment and neuronal and retinal degeneration. Clinically, the mutant on a C57Bl/6 genetic background shows a progressive motor abnormality starting by 6 months of age, with death prior to 12 months. When mnd is outcrossed to the AKR/J...

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Source

Identifiers

PMID: 10191135
DOI: 10.1006/mgme.1999.2817

Genes

NCL

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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