Article

Distinctive properties of the prion protein in the brain and retina in the amyloidosis associated with the PRNP F198S Mutation. *

2026-07-16

Abstract excerpt

<title>Abstract</title> <p>Prion protein (PrP) deposits in the form of diffuse and cored plaques occur in most gray matter areas of the brain of individuals affected by Gerstmann-Sträussler-Scheinker disease (GSS) associated with the F198S mutation in PRNP; however, the PrP deposits in the retina have not been characterized. Furthermore, a comparative analysis of PrP deposits occurring in the brain and in the ret...

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Literature Corpus work: 756510a6-8973-5828-8bc7-ec39a0586de7
DOI: 10.21203/rs.3.rs-9441514/v1

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