Article

Fatal Nodular Regenerating Hyperplasia Rupture in a Common-Variable-Immunodeficiency Patient With TACI Mutation

2021-05-06

Abstract excerpt

<title>Abstract</title> <p>BackgroundNodular regenerating hyperplasia (NRH) is considered the most common liver involvement in common variable immunodeficiency (CVID). Most patients are asymptomatic with gradually increasing alkaline phosphatase (ALP) and mildly elevated transaminase enzymes over years. We report the first case of fatal NRH rupture complication in a CVID patient.Case presentationA 24-year-old man...

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Literature Corpus work: 4b39f804-9e53-5e61-9d0a-c3b787c0e6dc
DOI: 10.21203/rs.3.rs-470039/v1

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