Article
Nodular regenerative hyperplasia in X-linked agammaglobulinemia: An underestimated and severe complication.
The Journal of allergy and clinical immunology - 1 Jan 2022
Nunes-Santos Cristiane J, Koh Christopher, Rai Anjali, Sacco Keith, Marciano Beatriz E, Kleiner David E, Marko Jamie, Bergerson Jenna R E, Stack Michael, Rivera Maria M, Constantine Gregory, Strober Warren, Uzel Gulbu, Fuss Ivan J, Notarangelo Luigi D, Holland Steven M, Rosenzweig Sergio D, Heller Theo
Abstract excerpt
BACKGROUND: Late-onset complications in X-linked agammaglobulinemia (XLA) are increasingly recognized. Nodular regenerative hyperplasia (NRH) has been reported in primary immunodeficiency but data in XLA are limited. OBJECTIVES: This study sought to describe NRH prevalence, associated features, and impact in patients with XLA. METHODS: Medical records of all patients with XLA referred to the National Institutes...
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