Article

A Case of Pleuroparenchymal Fibroelastosis Without Radiological Pleural Involvement

2025-11-10

Abstract excerpt

<title>Abstract</title> <p> <bold>Background</bold> Pleuroparenchymal fibroelastosis (PPFE) is a rare interstitial lung disease (ILD) characterised by elastosis and fibrosis of the pleura and adjacent subpleural lung parenchyma, generally involving the upper lobes. Atypical presentations have been described with a predominantly (intra-alveolar) airway-centred fibroelastosis without overt pleural involvement, co...

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Literature Corpus work: 1992a51f-a954-5e88-81f0-e270ee708f61
DOI: 10.21203/rs.3.rs-7913073/v1

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