Article

Pleuropulmonary Blastoma: A Single-center Case Series of 7 Patients

2020-12-20

Abstract excerpt

<h4>Introduction: </h4> Pleuropulmonary blastoma (PPB) is an aggressive primary neoplasm of pleuropulmonary mesenchyme occurring in children. Given its rarity, the International Pleuropulmonary Blastoma Registry (IPPBR) was established in 1988 to collect and assess data on PPB worldwide. We assessed the clinical characteristics, histopathology, genetic studies, management, and treatment outcomes of patients with P...

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Literature Corpus work: 093a63cb-7048-569b-8c26-f80a4d65d1b1
DOI: 10.22541/au.160849831.12668324/v1

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