Discover Community Create You

Loading publication...

Noodle always counts identifier-free feature events for service operation. With your permission, Google Analytics can also estimate audience and engagement. Search text, publication identifiers, cookies, IP addresses and browser fingerprints are never included in Noodle's first-party event counters.

Privacy details

Article

Clinical features of idiopathic pleuroparenchymal fibroelastosis with progressive phenotype showing a decline in forced vital capacity.

Respiratory investigation - 1 Mar 2023

Kono Masato, Tsunoda Tomo, Ikeda Shin, Yagi Shota, Hirama Ryutaro, Watanuki Masayuki, Oshima Yuiko, Tsutsumi Akari, Miwa Hideki, Miki Yoshihiro, Hashimoto Dai, Suda Takafumi, Nakamura Hidenori

Abstract excerpt

BACKGROUND: Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is heterogeneous, with some patients showing a progressive decline in forced vital capacity (FVC). However, the clinical features of these cases with progressive phenotypes remain unknown. METHODS: This retrospective study included 48 patients diagnosed with IPPFE who underwent longitudinal pulmonary function tests at our institution from 2005 to...

Read the complete abstract on PubMed

Topics

Share this publication in a Topic to start or enrich a Post.

Share to Idiopathic Pulmonary Fibrosis
Share to Lung

Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

Share to Phenotype

Share to Vital Capacity

Source

Identifiers

PMID: 36773509
DOI: 10.1016/j.resinv.2023.01.003

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

Related research

Semantic proximity does not establish scientific evidence.

Research trail→

Click a neighbor to travelStep 1 · 12 closest

Clinical features of idiopathic pleuroparenchymal fibroelastosis with progressive phenotype showing a decline in forced vital capacity.PMID 36773509Read ↗

Prevalence and prognosis of chronic fibrosing interstitial lung diseases with a progressive phenotype.Semantic proximity Read ↗

Upper lung asymmetry identifies distinct clinical phenotypes in idiopathic pleuroparenchymal fibroelastosis.Semantic proximity Read ↗

Idiopathic pulmonary fibrosis: phenotypes and comorbidities.Semantic proximity Read ↗

A syndromic framework for progressive pulmonary fibrosis.Semantic proximity Read ↗

A Case of Pleuroparenchymal Fibroelastosis Without Radiological Pleural InvolvementSemantic proximity Read ↗

The burden of Progressive Fibrotic Interstitial lung disease across the UKSemantic proximity Read ↗

An IPF-like disease course in disorders other than IPF: how can this be anticipated, recognized, and managed?Semantic proximity Read ↗

Compare three diagnostic criteria of progressive pulmonary fibrosisSemantic proximity Read ↗

An Aetiological and Observational Cohort study of Interstitial Lung Abnormalities (ILAs) Including Progressive Fibrosing Phenotype Interstitial Lung Diseases in a Large General Medical Check-up Population (Kumamoto ILA study in Japan) (KILA-J)Semantic proximity Read ↗

Retrospective analysis of the clinical features and prognosis of idiopathic pulmonary fibrosis combined with lung cancerSemantic proximity Read ↗

Focal Usual Interstitial Pneumonia-like Fibrosis is a Core Prognostic Factor in Progressive Pulmonary FibrosisSemantic proximity Read ↗

Progressive fibrosing interstitial lung disease: prevalence and clinical outcome.Semantic proximity Read ↗

⌁Select a neighboring publication to make it the new centre.