Article
Pleuroparenchymal fibroelastosis: a spectrum of histopathological and imaging phenotypes.
The European respiratory journal - 1 Aug 2012
Reddy Taryn L, Tominaga Masaki, Hansell David M, von der Thusen Jan, Rassl Doris, Parfrey Helen, Guy Suzy, Twentyman Orion, Rice Alexandra, Maher Toby M, Renzoni Elisabetta A, Wells Athol U, Nicholson Andrew G
Abstract excerpt
Pleuroparenchymal fibroelastosis (PPFE) is a rare condition characterised by predominantly upper lobe pleural and subjacent parenchymal fibrosis, the latter being intra-alveolar with accompanying elastosis of the alveolar walls. The aim of this study was to review cases fulfilling published imaging and histological criteria, and identify any common clinical features that may suggest an underlying aetiology for a...
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