Article

Hemophagocytic Lymphohistiocytosis Secondary to Macrophage Activation Syndrome in Adult-Onset Still’s Disease: A Diagnostic and Therapeutic Challenge

2025-06-04

Abstract excerpt

Hemophagocytic Lymphohistiocytosis (HLH) is a rare and serious syndrome characterized by excessive inflammation and tissue damage due to abnormal immune activation. It presents in two main forms: a genetic variant predominantly affecting children, and an acquired form more common in adults, often secondary to infections, malignancies, or autoimmune diseases such as systemic lupus erythematosus (SLE). Macrophage Ac...

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Literature Corpus work: 17047d7e-2c6f-5767-b89a-8bb3df5849fc
DOI: 10.20944/preprints202506.0350.v1

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