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Article

Recurrent hematuria: a novel clinical presentation of hereditary complete complement C4 deficiency.

American journal of kidney diseases : the official journal of the National Kidney Foundation - 1 Mar 1996

Lhotta K, Neunhauserer M, Solder B, Uring-Lambert B, Wurzner R, Rumpelt H J, Konig P

Abstract excerpt

A 10-year-old boy suffered from recurrent attacks of fever, vomiting, and hematuria. During disease flares, circulating immune complexes were detected in the serum. Elevated levels of Bb, Ba, and C3a indicated complement activation through the alternative pathway. Complement C4 was undetectable. C4 phenotyping by agarose gel electrophoresis showed complete C4 deficiency. Restriction fragment length polymorphism...

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Identifiers

PMID: 8604713
DOI: 10.1016/s0272-6386(96)90367-4

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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