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Article

Case report: Double-lung transplantation for Hermansky-Pudlak syndrome-associated pulmonary fibrosis and early-stage lung cancer.

Frontiers in immunology - 1 Jan 2026

Li Xiaotong, Ding Liangxia, Li Bin, Ding Zhaolei, Wang Kun, Li Junjuan, Gao Xiaopeng

Abstract excerpt

Lung transplantation for lung cancer remains exploratory but may benefit patients with concurrent end-stage lung disease. We present a 47-year-old Asian male with Hermansky-Pudlak syndrome-associated pulmonary fibrosis (HPS-PF), a congenital right-sided aortic arch, and a MUC5B mutation-an exceptionally rare case of multifactorial pulmonary fibrosis complicated by lung cancer. Preoperatively, he exhibited rapid...

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Identifiers

PMID: 41953037
DOI: 10.3389/fimmu.2026.1684523
PMCID: PMC13053257

Genes

MUC5B

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 8 Sept 2026.

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