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Article

Chemical chaperone 4-phenylbutyrate treatment alleviates the kidney phenotype in a mouse model of Alport syndrome with a pathogenic variant in Col4a3

6 Jun 2025

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

Identifiers

PMID: 40484355
DOI: 10.1016/j.kint.2025.05.016

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Chemical chaperone 4-phenylbutyrate treatment alleviates the kidney phenotype in a mouse model of Alport syndrome with a pathogenic variant in Col4a3PMID 40484355Read ↗

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The chemical chaperone 4-phenylbutyric acid rescues molecular cell defects of <i>COL3A1</i> mutations that cause vascular Ehlers Danlos SyndromeSemantic proximity Read ↗

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