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Article

Macrophage activation syndrome associated with griscelli syndrome type 2: case report and review of literature.

The Pan African medical journal - 1 Jan 2018

Sefsafi Zakia, Hasbaoui Brahim El, Kili Amina, Agadr Aomar, Khattab Mohammed

Abstract excerpt

Macrophage activation syndrome (MAS) is a severe and potentially fatal life-threatening condition associated with excessive activation and expansion of T cells with macrophages and a high expression of cytokines, resulting in an uncontrolled inflammatory response, with high levels of macrophage colony-stimulating factor and causing multiorgan damage. This syndrome is classified into primary (genetic/familial) or...

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Identifiers

PMID: 29875956
DOI: 10.11604/pamj.2018.29.75.12353
PMCID: PMC5987098

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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