Article
Diagnosing haemophagocytic syndrome.
Archives of disease in childhood - 1 Mar 2017
Sen Ethan S, Steward Colin G, Ramanan Athimalaipet V
Abstract excerpt
Haemophagocytic syndrome, or haemophagocytic lymphohistiocytosis (HLH), is a hyperinflammatory disorder characterised by uncontrolled activation of the immune system. It can result from mutations in multiple genes involved in cytotoxicity or occur secondary to a range of infections, malignancies or autoimmune rheumatic diseases. In the latter case, it is also known as macrophage activation syndrome (MAS)....
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.