Article
Polycystic liver disease: a clinical review.
Annals of hepatology - 1 Jan 2000
Chandok Natasha
Abstract excerpt
Polycystic liver disease rarely occurs in isolation as part of autosomal dominant polycystic liver disease, but more commonly, it exists as an extra-renal manifestation of autosomal dominant polycystic kidney disease. The pathogenesis of polycystic liver disease involves defects in the primary cilium of the cholangiocyte, with genetic mutations that impair key proteins integral to the complex functioning of...
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