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Article

Atypical neuropathological sCJD-MM phenotype with abundant white matter Kuru-type plaques sparing the cerebellar cortex.

Neuropathology : official journal of the Japanese Society of Neuropathology - 1 Apr 2013

Gelpi Ellen, Soler Insa Josep Ma, Parchi Piero, Saverioni Daniela, Yagüe Jordi, Nos Carlos, Martínez-Saez Elena, Ribalta Teresa, Ferrer Isidre, Sanchez-Valle Raquel

Abstract excerpt

We describe an atypical neuropatholgical phenotype of sporadic Creutzfeldt-Jakob disease (sCJD) in a 64-year-old man presenting with a 5-month history of rapidly progressive dementia, comprising behavioral disturbances, memory complaints, disorientation and language alterations. MRI showed diffuse atrophy and hyperintensities in parietal, occipital, temporal and frontal cortices and left caudate nucleus on...

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PMID: 22862687
DOI: 10.1111/j.1440-1789.2012.01341.x

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PRNP

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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