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Article

Atypical neuropathological sCJD-MM phenotype with abundant white matter Kuru-type plaques sparing the cerebellar cortex.

Neuropathology : official journal of the Japanese Society of Neuropathology - 1 Apr 2013

Gelpi Ellen, Soler Insa Josep Ma, Parchi Piero, Saverioni Daniela, Yagüe Jordi, Nos Carlos, Martínez-Saez Elena, Ribalta Teresa, Ferrer Isidre, Sanchez-Valle Raquel

Abstract excerpt

We describe an atypical neuropatholgical phenotype of sporadic Creutzfeldt-Jakob disease (sCJD) in a 64-year-old man presenting with a 5-month history of rapidly progressive dementia, comprising behavioral disturbances, memory complaints, disorientation and language alterations. MRI showed diffus...

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Identifiers

PMID: 22862687
DOI: 10.1111/j.1440-1789.2012.01341.x

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PRNP

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 4 Sept 2026. Prepared record publication-22862687-2026-09-04.2. Manifest publication-graph-cohort-2026-09-04.2.

Source receipt: PubMed via Helena Literature Corpus, retrieved 4 Sept 2026.

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