Article
Congenital aggressive variant of Langerhans cells histiocytosis with CD56+/E-Cadherin- phenotype.
Pediatric blood & cancer - 1 Dec 2009
Lucioni Marco, Beluffi Giampiero, Bandiera Laura, Zecca Marco, Inzani Frediano, Fiandrino Giacomo, Viglio Alessandra, Stronati Mauro, Necchi Vittorio, Riboni Roberta, Locatelli Franco, Paulli Marco
Abstract excerpt
In children < 2 years of age, cutaneous involvement is the most frequent presentation of Langerhans cell histiocytosis (LCH). Cutaneous LCH can be localized or associated with dissemination and organ dysfunction. The clinical course is variable, ranging from spontaneous regression to a fatal outcome. We describe a female newborn presenting with congenital cutaneous lesions who rapidly developed pulmonary...
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