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Article

Intracortical inhibition of the motor cortex in Segawa disease (DYT5).

Neurology - 27 Mar 2007

Hanajima R, Nomura Y, Segawa M, Ugawa Y

Abstract excerpt

BACKGROUND: Segawa disease (autosomal dominant guanosine triphosphate cyclohydrolase I [GTP-I] deficiency, DYT5) is a hereditary dopa-responsive generalized dystonia. OBJECTIVE: To investigate the pathophysiologic mechanisms for dystonia in Segawa disease, we studied intracortical inhibition of the primary motor cortex in patients with Segawa disease. METHODS: We studied 9 patients with Segawa disease (8...

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PMID: 17389309
DOI: 10.1212/01.wnl.0000257816.92101.54

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AMT

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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