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Article

Fibrillins 1 and 2 perform partially overlapping functions during aortic development.

The Journal of biological chemistry - 24 Mar 2006

Carta Luca, Pereira Lygia, Arteaga-Solis Emilio, Lee-Arteaga Sui Y, Lenart Brett, Starcher Barry, Merkel Christian A, Sukoyan Marina, Kerkis Alexander, Hazeki Noriko, Keene Douglas R, Sakai Lynn Y, Ramirez Francesco

Abstract excerpt

Fibrillin-rich microfibrils are extracellular assemblies that impart structural properties to the connective tissue. To elucidate the contribution of fibrillin-rich microfibrils to organogenesis, we have examined the vascular phenotype of a newly created strain of mice that completely lacks fibri...

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Identifiers

PMID: 16407178
DOI: 10.1074/jbc.M511599200
PMCID: PMC3052983

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 4 Sept 2026. Prepared record publication-16407178-2026-09-04.2. Manifest publication-graph-cohort-2026-09-04.2.

Source receipt: PubMed via Helena Literature Corpus, retrieved 4 Sept 2026.

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