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Article

Protein aggregation in motor neurone disorders.

Neuropathology and applied neurobiology - 1 Dec 2003

Wood J D, Beaujeux T P, Shaw P J

Abstract excerpt

Toxicity associated with abnormal protein folding and protein aggregation are major hypotheses for neurodegeneration. This article comparatively reviews the experimental and human tissue-based evidence for the involvement of such mechanisms in neuronal death associated with the motor system disorders of X-linked spinobulbar muscular atrophy (SBMA; Kennedy's disease) and amyotrophic lateral sclerosis (ALS),...

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Identifiers

PMID: 14636160
DOI: 10.1046/j.0305-1846.2003.00518.x

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SOD1

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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