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Article

Nerve conduction abnormalities and neuromyotonia in genetically engineered mouse models of human hereditary neuropathies.

Annals of the New York Academy of Sciences - 14 Sept 1999

Zielasek J, Toyka K V

Abstract excerpt

We performed electrophysiological studies in myelin protein mutant mice in order to characterize nerve conduction changes. We performed neurographic studies on the facial and sciatic nerves and needle electromyography (EMG). Mice homozygously deficient for the peripheral myelin protein 22 gene (P...

Topics

Animals
Axons
Charcot-Marie-Tooth Disease
Genotype
Humans
Mice
Mice, Knockout
Mice, Neurologic Mutants
Muscle, Skeletal
Myelin P0 Protein
Myelin Proteins
Myelin Sheath

Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

Neural Conduction

Source

Identifiers

PMID: 10586256

Genes

PMP22

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 31 Aug 2026. Prepared record publication-10586256-2026-08-31.1. Manifest publication-graph-cohort-2026-08-31.1.

Source receipt: PubMed via Helena Literature Corpus, retrieved 31 Aug 2026.

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Nerve conduction abnormalities and neuromyotonia in genetically engineered mouse models of human hereditary neuropathies.PMID 10586256Read ↗

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