Article
Liver transplantation for end-stage liver disease associated with alpha-1-antitrypsin deficiency in children: pretransplant natural history, timing and results of transplantation.
Journal of hepatology - 1 Jan 1994
Filipponi F, Soubrane O, Labrousse F, Devictor D, Bernard O, Valayer J, Houssin D
Abstract excerpt
Alpha-1-antitrypsin deficiency is an inborn metabolism error which can cause emphysema and liver disease. As regards the pathophysiology of liver disease, this deficiency is poorly understood, and it is also not known why only a small proportion of Pi ZZ individuals progress towards cirrhosis and...
Topics
- Child
- Female
- Follow-Up Studies
- Humans
- Liver Failure
- Liver Transplantation
- Male
- Metabolism, Inborn Errors
- Phenotype
- Retrospective Studies
- Time Factors
- Treatment Outcome
- alpha 1-Antitrypsin Deficiency