Loading publication...

Noodle always counts identifier-free feature events for service operation. With your permission, Google Analytics can also estimate audience and engagement. Search text, publication identifiers, cookies, IP addresses and browser fingerprints are never included in Noodle's first-party event counters.

Privacy details

Article

Fibrillin-containing microfibrils: structure and function in health and disease.

The international journal of biochemistry & cell biology - 1 Aug 1995

Kielty C M, Shuttleworth C A

Abstract excerpt

Fibrillin-containing microfibrils are a unique class of connective tissue macromolecules whose critical contribution to the establishment and maintenance of diverse extracellular matrices was underlined by the recent linkage of their principal structural component fibrillin to Marfan syndrome, a...

Topics

Connective Tissue
Extracellular Matrix Proteins
Fibrillins
Genotype
Humans
Marfan Syndrome
Microfilament Proteins
Phenotype
Reference Values
Structure-Activity Relationship

Source

Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

Identifiers

PMID: 7584608
DOI: 10.1016/1357-2725(95)00028-n

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 30 Aug 2026. Prepared record publication-7584608-2026-08-30.1. Manifest publication-graph-cohort-2026-08-30.1.

Source receipt: PubMed via Helena Literature Corpus, retrieved 30 Aug 2026.

Community interpretation

Discuss the evidence

Ask a question, add context or challenge an interpretation. Community activity is separate from scientific evidence strength.

0

discussions

0

replies

Citations encouraged

Claims remain attributable.

No discussion yet

Be the first to add a careful, cited interpretation.

Related research

Semantic proximity does not establish scientific evidence.

Research trail→

Click a neighbor to travelStep 1 · 12 closest

Fibrillin-containing microfibrils: structure and function in health and disease.PMID 7584608Read ↗

Microfibrils: a cornerstone of extracellular matrix and a key to understand Marfan syndrome.Semantic proximity Read ↗

The fibrillin-Marfan syndrome connection.Semantic proximity Read ↗

New insights into the structure, assembly and biological roles of 10-12 nm connective tissue microfibrils from fibrillin-1 studies.Semantic proximity Read ↗

Fibrillin‐rich microfibrils: Structural determinants of morphogenetic and homeostatic eventsSemantic proximity Read ↗

The extracellular matrix glycoprotein fibrillin-1 in health and diseaseSemantic proximity Read ↗

The molecular genetics of Marfan syndrome and related microfibrillopathies.Semantic proximity Read ↗

Fibrillin assemblies: extracellular determinants of tissue formation and fibrosisSemantic proximity Read ↗

The Multiple Functions of Fibrillin-1 Microfibrils in Organismal Physiology.Semantic proximity Read ↗

Fibrillin microfibril structure identifies long-range effects of inherited pathogenic mutations affecting a key regulatory TGFβ-binding siteSemantic proximity Read ↗

Dissecting the fibrillin microfibril: structural insights into organization and function.Semantic proximity Read ↗

FBN1: The disease-causing gene for Marfan syndrome and other genetic disorders.Semantic proximity Read ↗

Structural and functional failure of fibrillin‑1 in human diseases (Review)Semantic proximity Read ↗

⌁Select a neighboring publication to make it the new centre.