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Article

Over three decades of natural history of limb girdle muscular dystrophy type R1/2A and R2/2B: Mathematical modelling of a multifactorial study.

Neuromuscular disorders : NMD - 1 Jun 2021

LoMauro Antonella, Gandossini Sandra, Russo Annamaria, Diella Eleonora, Pistininzi Cristina, Marchi Eraldo, Pascuzzo Riccardo, Vantini Simone, Aliverti Andrea, D'Angelo Maria Grazia

Abstract excerpt

We aimed to describe the natural history of Limb Girdle Muscular Dystrophy type 2A and 2B over more than three decades by considering muscular strength, motor, cardiac and respiratory function. 428 visits of nineteen 2A and twenty 2B patients were retrospectively analysed through a regression model to create the curves of evolution with disease duration of muscle strength (through Medical Research Council...

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

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Identifiers

PMID: 33836912
DOI: 10.1016/j.nmd.2021.02.018

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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