Article
Twenty-one cases of blastic plasmacytoid dendritic cell neoplasm: focus on biallelic locus 9p21.3 deletion.
Blood - 27 Oct 2011
Lucioni Marco, Novara Francesca, Fiandrino Giacomo, Riboni Roberta, Fanoni Daniele, Arra Mariarosa, Venegoni Luigia, Nicola Marta, Dallera Elena, Arcaini Luca, Onida Francesco, Vezzoli Pamela, Travaglino Erica, Boveri Emanuela, Zuffardi Orsetta, Paulli Marco, Berti Emilio
Abstract excerpt
Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare and aggressive malignancy derived from precursors of plasmacytoid dendritic cells. We analyzed 21 cases with array-based comparative genomic hybridization (aCGH). Complete or partial chromosomal losses largely outnumbered the gains, with common deleted regions involving 9p21.3 (CDKN2A/CDKN2B), 13q13.1-q14.3 (RB1), 12p13.2-p13.1 (CDKN1B), 13q11-q12...
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