Article
Accessory spleen: differential diagnosis for lymphoma in autoimmune lymphoproliferative syndrome.
Pediatric blood & cancer - 1 Jul 2010
Georgin-Lavialle Sophie, Aouba Achille, Canioni Danielle, Rieux-Laucat Frédéric, Fischer Alain, Hermine Olivier
Abstract excerpt
Mutations of Fas or, less frequently, Fas ligand genes result in a rare inherited lymphoid disorder called autoimmune lymphoproliferative syndrome (ALPS) in which lymphoma frequency is increased. We report on a patient with ALPS who had been splenectomized for giant splenomegaly and progressively...
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.
