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rAAV6‐Microdystrophin Rescues Aberrant Golgi Complex Organization in <i>mdx </i>Skeletal Muscles

12 Jul 2007

Abstract excerpt

Muscular dystrophies are a diverse group of severe degenerative muscle diseases. Recent interest in the role of the Golgi complex (GC) in muscle disease has been piqued by findings that several dystrophies result from mutations in putative Golgi-resident glycosyltransferases. Given this new role of the Golgi in sarcolemmal stability, we hypothesized that abnormal Golgi distribution, regulation and/or function may...

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PMID: 17714427
DOI: 10.1111/j.1600-0854.2007.00622.x

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