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Article

Extraocular muscle is spared despite the absence of an intact sarcoglycan complex in gamma- or delta-sarcoglycan-deficient mice.

Neuromuscular disorders : NMD - 1 Mar 2001

Porter J D, Merriam A P, Hack A A, Andrade F H, McNally E M

Abstract excerpt

Models of the dystrophin-glycoprotein complex do not reconcile the novel sparing of extraocular muscle in muscular dystrophy. Extraocular muscle sparing in Duchenne muscular dystrophy implies the existence of adaptive properties in these muscles that may extend protection to other neuromuscular diseases. We studied the extraocular muscle morphology and dystrophin-glycoprotein complex organization in murine...

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Source

Identifiers

PMID: 11257478
DOI: 10.1016/s0960-8966(00)00171-1

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 5 Sept 2026. Manifest publication-graph-cohort-2026-09-05.1.

Source receipt: pubmed, retrieved 5 Sept 2026.

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Extraocular muscle is spared despite the absence of an intact sarcoglycan complex in gamma- or delta-sarcoglycan-deficient mice.PMID 11257478Read ↗

The sparing of extraocular muscle in dystrophinopathy is lost in mice lacking utrophin and dystrophinSemantic proximity Read ↗

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