Article

Carbamazepine-responsive Double-Negative VGKC-Complex Antibody Isaac’s Syndrome – A Case Report and Literature Review

2024-02-13

Abstract excerpt

<title>Abstract</title> <p><bold>Introduction. </bold>Isaacs syndrome (IS), commonly referred to as acquired neuromyotonia, is a rare condition characterized mainly by VGKC antibody-mediated syndrome of peripheral nerve hyperexcitability (PNH). Few case reports have documented IS patients in the absence of both LGI1 and CASPR2 antibodies (double-negative). <bold>Case Presentation. </bold>We report a rare case of...

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Literature Corpus work: f5001658-3f95-520c-adf9-bdc301736026
DOI: 10.21203/rs.3.rs-3921849/v1

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