Article

Modeling the cell biology of PEX11β deficiency during human neurogenesis

2026-02-16

Abstract excerpt

Peroxisomes are highly specialized organelles that are important for various metabolic functions, including β-oxidation of very-long-chain fatty acids and the synthesis of plasmalogens. Mutations in peroxisomal biogenesis proteins cause Zellweger spectrum disorders (ZSD), rare multisystem disorders often associated with neurological phenotypes. Unlike other peroxisome biogenesis proteins, PEX11β regulates peroxiso...

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Literature Corpus work: e8844ed9-fdc0-545f-b55d-453f7dafcde5
DOI: 10.64898/2026.02.13.705842

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