Article

Fatal JC-virus Granular Cerebellar Neuronopathy associated with Autoimmune Lymphoproliferative Syndrome and Common Variable Immunodeficiency

2020-09-30

Abstract excerpt

<title>Abstract</title> <p><bold>Background: </bold>JC-virus (JCV) associated granular cerebellar neuronopathy (JCV-GCN), which causes severe ataxia, is a rare complication of severe immunodeficiency and caused by a variant of JCV with a VP1-deletion. JCV-GCN has not yet been reported in patients with autoimmune lymphoproliferative syndrome (ALPS-FAS). We report a 34-year old woman with autoimmune lymphoprolifera...

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Literature Corpus work: cc4dd4a5-699d-56ed-8952-2129b2ec3503
DOI: 10.21203/rs.3.rs-81384/v1

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