Article
Nonidiopathic pleuroparenchymal fibroelastosis with a novel fibrillin-2 gene variant characterized by the expression of prenatal fibrillin-2 antigen and the aberrant proliferation of elastin and reticular fibers: a case report
2023-03-01
Abstract excerpt
<title>Abstract</title> <p> Pleuroparenchymal fibroelastosis is a recently recognized clinical entity characterized by interstitial pneumonia that has pathological characteristics with proliferating elastin in the upper lung regions. Pleuroparenchymal fibroelastosis is categorized as idiopathic or nonidiopathicdepending on coexistent initiating factors; however, congenital contractural arachnodactyly, which is c...
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Identifiers and source
- Literature Corpus work
- 9f8d96c1-cc86-5b82-86fb-29b7f04f9cc8
- DOI
- 10.21203/rs.3.rs-2012080/v2