Article
Pleuropulmonary Blastoma: Evolution of an Entity as an Entry into a Familial Tumor Predisposition Syndrome.
Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology Society - 1 Jan 2000
Dehner Louis P, Messinger Yoav H, Schultz Kris Ann P, Williams Gretchen M, Wikenheiser-Brokamp Kathryn, Hill D Ashley
Abstract excerpt
Pleuropulmonary blastoma (PPB) is the most common primary malignant neoplasm of the lung in children. Like other solid dysontogenic neoplasms, this tumor typically presents before 7 years of age. The earliest manifestation is the presence of a lung cyst(s), which is usually recognized in the first year of life and is difficult to differentiate on the basis of imaging studies from non-neoplastic cysts of early...
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.