Article
Pulmonary function in children with homozygous alpha1-protease inhibitor deficiency.
European journal of pediatrics - 1 Jul 1996
Wiebicke W, Niggemann B, Fischer A
Abstract excerpt
UNLABELLED: Alpha1-protease inhibitor (alpha1-PI) deficiency is a well-recognized cause of emphysema in adults; however, the natural history of this disorder in children is unclear. Because of the paucity of data in the paediatric age group, we performed whole body plethysmography, spirometry, an...
Topics
- Adolescent
- Anthropometry
- Case-Control Studies
- Child
- Female
- Humans
- Male
- Matched-Pair Analysis
- Phenotype
- Respiratory Function Tests
- Respiratory Mechanics
- Statistics, Nonparametric
- alpha 1-Antitrypsin
- alpha 1-Antitrypsin Deficiency
