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Article

Altered binaural hearing in pre-ataxic and ataxic mutation carriers of spinocerebellar ataxia type 3.

Cerebellum (London, England) - 1 Feb 2024

Jacobi Heike, Andermann Martin, Faber Jennifer, Baumann Felicitas, Rupp André

Abstract excerpt

Brainstem degeneration is a prominent feature of spinocerebellar ataxia type 3 (SCA3), involving structures that execute binaural synchronization with microsecond precision. As a consequence, auditory processing may deteriorate during the course of disease. We tested whether the binaural "Huggins pitch" effect is suitable to study the temporal precision of brainstem functioning in SCA3 mutation carriers. We...

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PMID: 36715818
DOI: 10.1007/s12311-023-01519-3
PMCID: PMC10864462

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