Article
Nationwide retrospective observational study of idiopathic dendriform pulmonary ossification: clinical features with a progressive phenotype.
BMJ open respiratory research - 1 Sept 2022
Nishioka Yasuhiko, Toyoda Yuko, Egashira Ryoko, Johkoh Takeshi, Terasaki Yasuhiro, Hebisawa Akira, Abe Kinya, Baba Tomohisa, Fujikura Yuji, Fujita Etsuo, Hamada Naoki, Handa Tomohiro, Hasegawa Yoshinori, Hidaka Koko, Hisada Takeshi, Hisata Shu, Honjo Chisato, Ichikado Kazuya, Inoue Yoshikazu, Izumi Shinyu, Kato Motoyasu, Kishimoto Takumi, Okamoto Masaki, Miki Keisuke, Mineshita Masamichi, Nakamura Yutaro, Sakamoto Susumu, Sano Masaaki, Tsukada Yoshikazu, Yamasue Mari, Bando Yoshimi, Homma Sakae, Hagiwara Koichi, Suda Takafumi, Inase Naohiko
Abstract excerpt
BACKGROUND: Diffuse pulmonary ossification is a specific lung condition that is accompanied by underlying diseases. However, idiopathic dendriform pulmonary ossification (IDPO) is extremely rare, and the clinical features remain unclear. In this study, we aimed to report the clinical characteristics of IDPO. METHODS: We conducted a nationwide survey of patients with IDPO from 2017 to 2019 in Japan and evaluated...
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