Article

Respiratory oscillometry in individuals with fibrodysplasia ossificans progressiva

2025-05-06

Abstract excerpt

<title>Abstract</title> <p><bold>Background:</bold> Fibrodysplasia ossificans progressiva (FOP) is an ultra-rare genetic bone disease that is characterized by progressive heterotopic ossification of the thoracic cavity. Prognosis is poor with cardiopulmonary complications being the main cause of death. Spirometry is a well-established metric of functional exercise capacity and prognosis in lung diseases but its u...

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Literature Corpus work: d04972b4-6ce2-521a-a434-3f1b27cf9840
DOI: 10.21203/rs.3.rs-5753372/v1

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