Article
FHR-5 Serum Levels and CFHR5 Genetic Variations in Patients With Immune Complex-Mediated Membranoproliferative Glomerulonephritis and C3-Glomerulopathy.
Frontiers in immunology - 1 Jan 2021
Garam Nóra, Cserhalmi Marcell, Prohászka Zoltán, Szilágyi Ágnes, Veszeli Nóra, Szabó Edina, Uzonyi Barbara, Iliás Attila, Aigner Christof, Schmidt Alice, Gaggl Martina, Sunder-Plassmann Gere, Bajcsi Dóra, Brunner Jürgen, Dumfarth Alexandra, Cejka Daniel, Flaschberger Stefan, Flögelova Hana, Haris Ágnes, Hartmann Ágnes, Heilos Andreas, Mueller Thomas, Rusai Krisztina, Arbeiter Klaus, Hofer Johannes, Jakab Dániel, Sinkó Mária, Szigeti Erika, Bereczki Csaba, Janko Viktor, Kelen Kata, Reusz György S, Szabó Attila J, Klenk Nóra, Kóbor Krisztina, Kojc Nika, Knechtelsdorfer Maarten, Laganovic Mario, Lungu Adrian Catalin, Meglic Anamarija, Rus Rina, Kersnik Levart Tanja, Macioniene Ernesta, Miglinas Marius, Pawłowska Anna, Stompór Tomasz, Podracka Ludmila, Rudnicki Michael, Mayer Gert, Rysava Romana, Reiterova Jana, Saraga Marijan, Seeman Tomáš, Zieg Jakub, Sládková Eva, Stajic Natasa, Szabó Tamás, Capitanescu Andrei, Stancu Simona, Tisljar Miroslav, Galesic Kresimir, Tislér András, Vainumäe Inga, Windpessl Martin, Zaoral Tomas, Zlatanova Galia, Józsi Mihály, Csuka Dorottya
Abstract excerpt
Background: Factor H-related protein 5 (FHR-5) is a member of the complement Factor H protein family. Due to the homology to Factor H, the main complement regulator of the alternative pathway, it may also be implicated in the pathomechanism of kidney diseases where Factor H and alternative pathway dysregulation play a role. Here, we report the first observational study on CFHR5 variations along with serum FHR-5...
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