Article
Secondary hemophagocytic lymphohistiocytosis: a case report.
Acta bio-medica : Atenei Parmensis - 30 Apr 2021
Salvati Lia, Di Renzo Anita, Moscardelli Sergio, Natali Laura, Claudio Ferri, Viscido Angelo
Abstract excerpt
Hemophagocytic lymphohistiocytosis (HLH) is a rare hematologic syndrome presenting either as an inherited life-threatening inflammatory disorder in children or as a secondary disease in adults. Inherited HLH involves inborn defects in lymphocytes and includes autosomal recessive and X-linked disorders characterized by uncontrolled activation of T cells and macrophages and overproduction of inflammatory cytokines....
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