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Article

PET imaging analysis with 64Cu in disulfiram treatment for aberrant copper biodistribution in Menkes disease mouse model.

Journal of nuclear medicine : official publication, Society of Nuclear Medicine - 1 May 2014

Nomura Shiho, Nozaki Satoshi, Hamazaki Takashi, Takeda Taisuke, Ninomiya Eiichi, Kudo Satoshi, Hayashinaka Emi, Wada Yasuhiro, Hiroki Tomoko, Fujisawa Chie, Kodama Hiroko, Shintaku Haruo, Watanabe Yasuyoshi

Abstract excerpt

UNLABELLED: Menkes disease (MD), an X-linked recessive disorder of copper metabolism caused by mutations in the copper-transporting ATP7A gene, results in growth failure and severe neurodegeneration in early childhood. Subcutaneous copper-histidine injection is the standard treatment for MD, but...

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Identifiers

PMID: 24627433
DOI: 10.2967/jnumed.113.131797

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 4 Sept 2026. Prepared record publication-24627433-2026-09-04.2. Manifest publication-graph-cohort-2026-09-04.2.

Source receipt: PubMed via Helena Literature Corpus, retrieved 4 Sept 2026.

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