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Article

Prognostic implications of mutation-specific QTc standard deviation in congenital long QT syndrome.

Heart rhythm - 1 May 2013

Mathias Andrew, Moss Arthur J, Lopes Coeli M, Barsheshet Alon, McNitt Scott, Zareba Wojciech, Robinson Jennifer L, Locati Emanuela H, Ackerman Michael J, Benhorin Jesaia, Kaufman Elizabeth S, Platonov Pyotr G, Qi Ming, Shimizu Wataru, Towbin Jeffrey A, Michael Vincent G, Wilde Arthur A M, Zhang Li, Goldenberg Ilan

Abstract excerpt

BACKGROUND: Individual corrected QT interval (QTc) may vary widely among carriers of the same long QT syndrome (LQTS) mutation. Currently, neither the mechanism nor the implications of this variable penetrance are well understood. OBJECTIVES: To hypothesize that the assessment of QTc variance in patients with congenital LQTS who carry the same mutation provides incremental prognostic information on the...

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Identifiers

PMID: 23369741
DOI: 10.1016/j.hrthm.2013.01.032

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 5 Sept 2026. Manifest publication-graph-cohort-2026-09-05.1.

Source receipt: pubmed, retrieved 5 Sept 2026.

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