Article
Primary hemophagocytic lymphohistiocytosis in Iran: report from a single referral center.
Pediatric hematology and oncology - 1 Apr 2012
Shamsian Bibi Shahin, Rezaei Nima, Alavi Samin, Hedayat Mona, Amin Asnafi Ali, Pourpak Zahra, Gharib Atoosa, Jadali Farzaneh, Arzanian Mohammad Taghi
Abstract excerpt
Hemophagocytic lymphohistiocytosis (HLH) is a rare condition characterized by fever, hepatosplenomegaly, and cytopenia, and widespread accumulation of lymphocytes and histiocytes, sometimes with hemophagocytosis, primarily involving the spleen, lymph nodes, bone marrow, and liver. HLH can either occur sporadically (secondary HLH) or as part of a familial syndrome (primary HLH), including familial HLH and the...
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