Hyper IgE (Job's) syndrome: a primary immune deficiency with oral manifestations.

Abstract excerpt

Autosomal dominant hyper IgE (HIES or Job's) syndrome is a rare primary immune deficiency characterized by eczema, recurrent skin and lung infections, extremely elevated serum IgE, and a variety of connective tissue and skeletal abnormalities. Individuals with HIES share a characteristic facial appearance and many oral manifestations including retained primary dentition, a high arched palate, variations of the...

Topics

Share this publication in a Topic to start or enrich a Post.

• Share to Candidiasis, Oral
• Share to Facies
• Share to Job Syndrome