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Article

Protein-sensitive hypoglycemia without leucine sensitivity in hyperinsulinism caused by K(ATP) channel mutations.

The Journal of pediatrics - 1 Jul 2006

Fourtner Shannon H, Stanley Charles A, Kelly Andrea

Abstract excerpt

OBJECTIVE: Because children with congenital hyperinsulinism (HI) caused by recessive loss of function mutations in the adenosine triphosphate (ATP)-dependent potassium channel (K(ATP)-HI) are not leucine sensitive, we evaluated for protein-induced hypoglycemia with oral protein tolerance tests. STUDY DESIGN: Blood glucose and insulin concentrations were measured every 15 minutes for 3 hours after an oral protein...

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

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Share to Potassium Channels, Inwardly Rectifying

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Source

Identifiers

PMID: 16860127
DOI: 10.1016/j.jpeds.2006.02.033

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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