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Article

Developmental paradigm for early features of cystic fibrosis.

Pediatric pulmonology - 1 Nov 2005

Larson Janet E, Cohen J Craig

Abstract excerpt

Cystic fibrosis (CF) is a progressive disease in which the lung is perceived to be normal at birth and is injured by recurrent infection. However, there is increasing evidence that the lung is functionally and structurally abnormal prior to the appearance of clinical infection. The cystic fibrosis transmembrane regulator (CFTR) is highly expressed in fetal tissues, and this review examines the role of CFTR in...

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Identifiers

PMID: 15830387
DOI: 10.1002/ppul.20169

Genes

CFTR

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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