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Article

Insights into the molecular mechanisms of bradycardia-triggered arrhythmias in long QT-3 syndrome.

The Journal of clinical investigation - 1 Nov 2002

Clancy Colleen E, Tateyama Michihiro, Kass Robert S

Abstract excerpt

Congenital long QT syndrome is a rare disease in which the electrocardiogram QT interval is prolonged due to dysfunctional ventricular repolarization. Variant 3 (LQT-3) is associated with mutations in SCN5A, the gene coding for the heart Na(+) channel alpha subunit. Arrhythmias in LQT-3 mutation...

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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

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Identifiers

PMID: 12417563
DOI: 10.1172/JCI15928
PMCID: PMC151612

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 4 Sept 2026. Prepared record publication-12417563-2026-09-04.2. Manifest publication-graph-cohort-2026-09-04.2.

Source receipt: PubMed via Helena Literature Corpus, retrieved 4 Sept 2026.

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