Article
Short rib polydactyly syndrome type III: histopathogenesis of the skeletal phenotype.
Pediatric and developmental pathology : the official journal of the Society for Pediatric Pathology and the Paediatric Pathology Society - 1 Jan 2000
Corsi Alessandro, Riminucci Mara, Roggini Mario, Bianco Paolo
Abstract excerpt
A morphological study of the skeletal system in a case of short rib polydactyly syndrome type III (SRPS-III) documented a "bajonet" deformity of the ribs for misalignment and overlap of cartilaginous and bony ends. This deformity resulted from a 'tandem' change in endochondral bone formation that is, arrested orthotopic cartilage maturation and etherotopic perichondral cartilage differentiation and ossification....
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